Observational Study: Dermatofibrosarcoma Protuberans, Case Series.

Published

2019-12-31

How to Cite

Amaluisa, D., Ojeda, K., Agular, Y., Gallegos, J., Palacios, S., Caza, M., Pérez Tasigchana, F., Simancas Racines, D., & Viteri García, A. (2019). Observational Study: Dermatofibrosarcoma Protuberans, Case Series. Oncology Journal (Ecuador), 29(3), 179–188. https://doi.org/10.33821/461

Issue

Section

Original Articles

Authors

  • Diana Amaluisa Facultad de Ciencias de la Salud Eugenio Espejo. Posgrado de Dermatología. Universidad Tecnológica Equinoccial, Ecuador https://orcid.org/0000-0001-5088-7023
  • Karina Ojeda Facultad de Ciencias de la Salud Eugenio Espejo. Posgrado de Dermatología. Universidad Tecnológica Equinoccial, Ecuador https://orcid.org/0000-0001-8923-3457
  • Yadira Agular Facultad de Ciencias de la Salud Eugenio Espejo. Posgrado de Dermatología. Universidad Tecnológica Equinoccial, Ecuador
  • Jorge Gallegos Facultad de Ciencias de la Salud Eugenio Espejo. Posgrado de Dermatología. Universidad Tecnológica Equinoccial, Ecuador https://orcid.org/0000-0003-0310-3841
  • Santiago Palacios Instituto CEPI-Centro de la Piel, Quito, Ecuador
  • Mery Caza Facultad de Ciencias de la Salud Eugenio Espejo. Universidad Tecnológica Equinoccial, Quito, Ecuador https://orcid.org/0000-0001-7692-5964
  • Francisco Pérez Tasigchana Facultad de Ciencias de la Salud Eugenio Espejo. Centro de Epidemiología Clínica y Salud Pública (CISPEC), Universidad Técnica Equinoccial.
  • Daniel Simancas Racines Facultad de Ciencias de la Salud Eugenio Espejo. Centro de Epidemiología Clínica y Salud Pública (CISPEC), Universidad Técnica Equinoccial. https://orcid.org/0000-0002-3641-1501
  • Andrés Viteri García Universidad Universidad Técnica Equinoccial. Facultad de Ciencias de la Salud Eugenio Espejo. Centro de Epidemiología Clínica y Salud Pública (CISPEC). https://orcid.org/0000-0003-0393-2404

DOI:

https://doi.org/10.33821/461

Keywords:

DERMATOFIBROSARCOMA, SKIN, MOHS SURGERY, HISTIOCYTIC SARCOMA

Abstract

Introduction: Dermatofibrosarcoma protuberans (DFSP) is one of the rare tumors found in the fibrohistocytic sarcomas and it is characterized by slow and progressive growth.

Methods: A retrospective study of six cases treated at the Skin Center (CEPI) between 2010 and 2019 was carried out. We have take into account demographic information, characteristics, treatment and evolution of the lesions.

Results: Six patients were diagnosed and treated by DFSP. There was a predominance of women (4 women, 2 men) with a mean age of 58.2 (SD = 19.6), three of them presented lesions in the form of indurated plaque and the rest presented a unique nodule. The locations of the lesions were the shoulder, neck and hypogastrium. The most commonly used treatment was wide excision, none of the patients presented recurrences at the first and fifth year of follow-up.

Conclusion: Recognition of the typical clinical characteristics of DFSP is necessary since it could be mistaken as a benign tumor of the skin. The diagnosis must be always done by histopathological confirmation.

Downloads

Download data is not yet available.

Most read articles by the same author(s)