Abstract
Introduction: The primitive neuroectodermal tumor (PNET) of the thoracic wall also called Askin's tumor is a rare and aggressive neoplasm, affecting mainly children and adolescents.
Clinical case: We report the case of a 17-year-old boy who presented a large right subscapular tumor, accompanied by pain and dyspnea who underwent previous neoadjuvant chemotherapy and given good response, tumor resection with oncological margins plus plastic reconstruction of the right hemithorax. Being confirmed as an intraoperative finding, not evident in images, pulmonary metastasis. It presents favorable postoperative evolution with subsequent local recurrence and distant metastasis, without response to adjuvant chemotherapy with death 7 months after surgery.
Conclusion: In the present case, the TA had a short survival despite neoadjuvant treatment, surgical resection and a new cycle of chemotherapy treatment.